以發(fā)熱為首發(fā)臨床表現(xiàn)的緩解性血清陰性對稱性滑膜炎伴凹陷性水腫綜合征一例
摘要:緩解性血清陰性對稱性滑膜炎伴凹陷性水腫綜合征(RS3PE)是一種罕見的血清陰性關(guān)節(jié)滑膜炎性疾病,發(fā)熱是其少見癥狀,國內(nèi)罕見以發(fā)熱為首發(fā)臨床表現(xiàn)的RS3PE綜合征的病例報道。本文報道1例以發(fā)熱為首發(fā)癥狀并通過系統(tǒng)的發(fā)熱查因診斷為RS3PE綜合征的患者。
關(guān)鍵詞:緩解性血清陰性對稱性滑膜炎伴凹陷性水腫綜合征;發(fā)熱;雙下肢凹陷性水腫
中圖分類號: R593.2 文獻(xiàn)標(biāo)識碼: B 文章編號:1000-503X(2024)06-0970-04
DOI:10.3881/j.issn.1000-503X.15977
Remitting Seronegative Symmetrical Synovitis With Pitting Edema Syndrome With Fever as the First Clinical Manifestation:Report of One Case
ZHONG Tianchang1,F(xiàn)ANG Zihao2,WEN Yingyan2,LAI Kang’an3,LI Jiachun4
1Department of Emergency,Zhongshan Hospital of Traditional Chinese Medicine,Zhongshan,Guangdong 528400,China
2Department of Respiratory Medicine,The Eighth School of Clinical Medicine,Guangzhou University of Chinese Medicine,F(xiàn)oshan,Guangdong 528000,China
3Department of Geriatrics,Zhongshan Hospital of Traditional Chinese Medicine,Zhongshan,Guangdong 528400,China
4Department of Respiratory Medicine,F(xiàn)oshan Hospital of Traditional Chinese Medicine,F(xiàn)oshan,Guangdong 528000,China
Corresponding author:LI Jiachun Tel:0757-83066081,E-mail:398149605@qq.com
ABSTRACT:Remitting seronegative symmetrical synovitis with pitting edema (RS3PE) syndrome is a rare seronegative synovial inflammatory disease in which fever is a rare symptom.There are few case reports of RS3PE syndrome with fever as the first clinical manifestation in China.In this paper,we report a case of RS3PE syndrome with fever as the first symptom and diagnosed by systematic fever investigation.
Key words:remitting seronegative symmetrical synovitis with pitting edema syndrome;fever;pitting edema of both lower limbs
Acta Acad Med Sin,2024,46(6):970-973
緩解性血清陰性對稱性滑膜炎伴凹陷性水腫(remitting seronegative symmetrical synovitis with pitting edema,RS3PE)綜合征是一種主要累及四肢遠(yuǎn)端的血清陰性關(guān)節(jié)滑膜炎性疾病,其發(fā)病率低,缺乏特異性檢驗(yàn)、檢查指標(biāo),缺少相關(guān)診治指南,極易漏診、誤診。(剩余6644字)
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