巨型肝血管平滑肌脂肪瘤伴包膜下破裂誤診為肝細(xì)胞癌1例報告

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摘要：肝血管平滑肌脂肪瘤（HAML）是一種罕見的良性間充質(zhì)腫瘤，多發(fā)于中年女性，由于早期無明顯癥狀，且缺乏特異的影像學(xué)表現(xiàn)，因此，診斷難度大，誤診率高。本文報道1例巨型HAML伴包膜下破裂誤診為肝細(xì)胞癌的病例，介紹其病例特點和診治經(jīng)過，期望為此類疾病的診治提供參考。

關(guān)鍵詞：肝腫瘤；血管肌脂瘤；誤診

基金項目：山西醫(yī)科大學(xué)第一醫(yī)院博士基金項目（SYYYRC-2023016）

Rare giant hepatic angiomyolipoma with subcapsular rupture misdiagnosed as hepatocellular carcinoma：A case report

ZHANG Zhiwei 1 ，LIU Feng 2 ，ZHANG Hezhao 3，4a ，WANG Qinying 4b ，SHI Zhiyong 3，4a

1. The First Clinical Medical College of Shanxi Medical University，Taiyuan 030000，China；2. Department of Head and Neck Surgery，Shanxi Cancer Hospital，Shanxi Hospital Affiliated to Cancer Hospital，Chinese Academy of Medical Sciences，Cancer Hospital Affiliated to Shanxi Medical University，Taiyuan 030000，China；3. Institute of Liver Disease，Shanxi Medical University，Taiyuan 030000，China；4. a. Department of Hepatobiliary Surgery，b. Department of Infectious Diseases，The First Hospital of Shanxi Medical University，Taiyuan 030000，China

Corresponding author：SHI Zhiyong，shizhiyong2015@163.com （ORCID：0000-0001-8379-9847）

Abstract：Hepatic angiomyolipoma （HAML） is a rare benign mesenchymal tumor frequently observed in middle-aged women. Due to the absence of prominent symptoms in the early stage and the lack of specific imaging findings，the diagnosis of this disease can be challenging，leading to a high rate of misdiagnosis. This article reports a case of giant HAML with subcapsular rupture that was misdiagnosed as hepatocellular carcinoma and introduces the characteristics of the case and its diagnosis and treatment process，in order to provide a reference for the diagnosis and treatment of this type of disease.

Key words：Liver Neoplasms；Angiomyolipomas；Diagnostic Errors

Research funding：The First Hospital of Shanxi Medical University Doctoral Fund Project （SYYYRC-2023016）

肝 血 管 平 滑 肌 脂 肪 瘤（hepatic angiomyolipoma，HAML）是一種罕見的良性間充質(zhì)腫瘤，通常由血管、平滑肌細(xì)胞和成熟脂肪組織按不同比例組成［1］。（剩余12613字）